Childhood Central Nervous System Atypical Teratoid/Rhabdoid Tumor

Central nervous system (CNS) atypical teratoid/rhabdoid tumors (AT/RT) are very rare, fast-growing tumors of the brain and spinal cord that usually occur in children age 3 and younger, although it can occur in older children and adults.

About half of these tumors form in the cerebellum or brain stem. The cerebellum is the part of the brain that controls movement, balance, and posture. The brain stem controls breathing, heart rate, and the nerves and muscles used in seeing, hearing, walking, talking, and eating. AT/RT may also be found in other parts of the central nervous system – the brain and spinal cord.

Certain genetic changes may increase the risk of developing atypical teratoid/rhabdoid tumors.

Childhood Central Nervous System Atypical Teratoid/Rhabdoid Tumor Treatment (PDQ®)

Source: National Cancer Institute